392 - Patient whit West Syndrome and Autistic Spectrum Disorder: Case report

West syndrome (WS) is a severe form of epilepsy of idiopathic origin, which manifests in early childhood between 3 and 7 months of age, it is considered a malignant condition that is characterized by the triad of epileptic spasms, Delayed psychomotor development and electroencephalographic pattern of hypsarrhythmia on the electroencephalogram.  Autism spectrum disorder (ASD) is a neurodevelopmental disorder that affects the areas of social and behavioral communication, which can manifest as intellectual disability, developmental difficulties, psychological and behavioral disorders. The behavior management for this patient can be difficult but using the correct adaptation technique a successful dental treatment can be executed.

7-year-old female patient with West syndrome and autism spectrum disorder, attends dental evaluation at the Pediatric Dentistry postgraduate clinic of the Universidad Los Andes in 2023 for permanence of temporary teeth (5.1-6.1), Frankl 1. without history of previous dental care, with mixed dentition in the first phase.

The first part of the treatment consists of adaptation and patient management sessions first in the morning with an anticipation strategy, say show do and desensitization. The second phase consisted of the extraction of teeth 5.1 and 6.1 in dental boxes, Follow up every 3 months with fluoride application, oral hygiene instruction, dietary advice, and evaluation of tooth replacement.

This case demonstrates that it is important to consider the patient's systemic condition. West syndrome and autism spectrum disorder require a multidisciplinary approach where patient management is essential to provide the best possible dental treatment.

Identify Supporting Agency and Grant Number: